alglucerase

• CAT Number: M100684
• CAS Number: 143003-46-7
• Molecular Formula: C6H8N2O3
• Purity: ≥95%
• Storage: Desiccate at -20C

Alglucerase(CAT: M100684) is a modified form of the enzyme β-glucocerebrosidase used as an enzyme replacement therapy for Gaucher disease, a lysosomal storage disorder. It is derived from human placental tissue and is specifically designed to break down glucocerebroside, a lipid that accumulates in the cells of affected individuals. Alglucerase functions by hydrolyzing glucocerebroside into glucose and ceramide, thereby alleviating symptoms such as hepatosplenomegaly, anemia, and bone abnormalities. This therapeutic enzyme is crucial for managing Gaucher disease by improving cellular function and reducing pathological manifestations. Alglucerase has paved the way for more advanced enzyme therapies, offering targeted and effective treatment for lysosomal storage disorders.