Hexanoylglycine-d2

• CAT Number: S000611
• CAS Number: 1256842-52-0
• Molecular Formula: C8H13D2NO3
• Molecular Weight: 175.22
• Purity: ≥95%
• IUPAC Name: carboxymethyl-dideuterio-hexanoylazanium
• InChI: InChI=1S/C8H15NO3/c1-2-3-4-5-7(10)9-6-8(11)12/h2-6H2,1H3,(H,9,10)(H,11,12)/p+1/i/hD2
• InChIKey: UPCKIPHSXMXJOX-ZSJDYOACSA-O
• SMILES: CCCCCC(=O)[NH2+]CC(=O)O

Hexanoylglycine-d2（Cat No.:S000611） is a deuterium-labeled version of hexanoylglycine, where two hydrogen atoms are replaced with deuterium (D). This labeled compound is used primarily in diagnostic applications, particularly in the detection of metabolic disorders using mass spectrometry. Hexanoylglycine, a metabolite associated with fatty acid oxidation, plays a critical role in metabolic profiling, especially in identifying disorders like medium-chain acyl-CoA dehydrogenase deficiency (MCADD). By incorporating deuterium, Hexanoylglycine-d2 provides a stable, internal standard that enhances the accuracy and precision of quantitative analyses, crucial for effective diagnosis and monitoring of metabolic diseases.