Tiglyl carnitine

• CAT Number: I019794
• CAS Number: 64681-36-3
• Molecular Formula: C12H21NO4
• Molecular Weight: 243.30
• Purity: ≥95%
• Synonyms: (3R)-3-[(E)-2-methylbut-2-enoyl]oxy-4-(trimethylazaniumyl)butanoate
• InChI: InChI=1S/C12H21NO4/c1-6-9(2)12(16)17-10(7-11(14)15)8-13(3,4)5/h6,10H,7-8H2,1-5H3/b9-6+/t10-/m1/s1
• InChIKey: WURBQCVBQNMUQT-OLKPEBQYSA-N
• SMILES: CC=C(C)C(=O)OC(CC(=O)[O-])C[N+](C)(C)C

Tiglyl carnitine is found to be associated with celiac disease and mitochondrial acetoacetyl-CoA thiolase (T2) deficiency.

Reference

[1]. Fukao T, et al. The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activit
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